Biliary obstruction in infants with cystic fibrosis requiring Kasai portoenterostomy☆
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Cited by (16)
Biliary atresia and its mimics
2023, Diagnostic HistopathologyCitation Excerpt :Extrahepatic abnormalities in cystic fibrosis can mimic BA. There are reports of CF patients with neonatal cholestasis and “hypoplastic/atretic” biliary tract with successful relief of jaundice by Kasai portoenterostomy.60,61 A detailed pathologic study of 4 male infants undergoing Kasai portoenterostomy showed that despite gross or macroscopic similarities in the extrahepatic abnormalities in BA and CF, the microscopic examination was distinct with CF patients showing accumulation of mucus, distended peribiliary glands, and absence of inflammation or fibroplasia surrounding the bile ducts.62
52 - Nonpulmonary Manifestations of Cystic Fibrosis
2019, Kendig's Disorders of the Respiratory Tract in ChildrenLiver disease in cystic fibrosis
2018, Practical Hepatic Pathology: A Diagnostic Approach: Second EditionCholestasis as the first symptom of gallbladder hypoplasia
2016, Cirugia EspanolaCystic Fibrosis
2011, Practical Hepatic Pathology: A Diagnostic Approach A Volume in the Pattern Recognition Series, Expert Consult: Online and PrintCystic Fibrosis
2011, Practical Hepatic Pathology
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Presented at the 27th Annual Meeting of the American Pediatric Surgical Association, San Diego, California, May 20–23, 1996.
Copyright © 1997 Published by Elsevier Inc.