Paralisi sopranucleare progressiva (malattia di Steele-Richardson-Olszewski)

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La paralisi sopranucleare progressiva (PSP o malattia di Steele-Richardson-Olszewski) è la seconda causa in ordine di frequenza di parkinsonismo, dopo la morbo di Parkinson. L’età di esordio media è di 60 anni. È caratterizzata da acinesia assiale, paralisi della verticalità dello sguardo, distonia cervicale in estensione, sindrome pseudobulbare e sindrome sotto-corticofrontale. La conferma della diagnosi spetta allo studio neuropatologico, con una perdita neuronale e degenerazioni neurofibrillari del tronco cerebrale.

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