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Successful Use of Recombinant Factor VIIa (NovoSeven) During Cardiac Surgery in a Pediatric Patient with Glanzmann Thrombasthenia

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Abstract

Glanzmann thrombasthenia is a rare, hereditary, congenital disorder of platelet function characterized by inappropriate bleeding that is difficult to control. Recombinant activated factor VII (rFVIIa) is a new treatment that is used to stop bleeding and provide surgical support for these patients. This report describes the use of rFVIIa to prevent serious bleeding during and after open-heart surgery in a child with Glanzmann thrombasthenia.

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Correspondence to N. Ozbek.

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Yilmaz, B., Alioglu, B., Ozyurek, E. et al. Successful Use of Recombinant Factor VIIa (NovoSeven) During Cardiac Surgery in a Pediatric Patient with Glanzmann Thrombasthenia. Pediatr Cardiol 26, 843–845 (2005). https://doi.org/10.1007/s00246-004-0919-7

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  • DOI: https://doi.org/10.1007/s00246-004-0919-7

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