Résumé
Le Purpura thrombopénique idiopathique (PTI) est l’étiologie la plus souvent retenue lors de la découverte d’une thrombopénie chez l’enfant, âgé de deux à dix ans, en bonne santé. Il se révèle le plus souvent par un syndrome hémorragique aigu, le plus souvent bénin, à prédominance cutanéomuqueuse. Les complications hémorragiques sévères sont rares. Il existe cependant des présentations atypiques, imposant d’éliminer les diagnostics différentiels: nous rapportons le cas d’un nourrisson ayant présenté un syndrome hémorragique sévère, avec hémorragie cérébrale sans atteinte cutanée, attribué par élimination à un PTI.
Asbstract
ITP is the aetiology most often considered when thrombocytopaenia is discovered in healthy children, aged between 2 and 10 years. It presents most often as acute haemorrhagic syndrome, usually not serious, predominantly in the skin and mucous membranes. Severe haemorrhagic complications are rare. However, there are atypical presentations, requiring different diagnoses to be ruled out: we are reporting on the case of an infant who presented with severe haemorrhagic syndrome, with cerebral haemorrhaging not affecting the skin, and by the process of elimination, it was attributed to ITP.
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Aurégan, C., Touzot, F., Grévent, D. et al. Purpura thrombopénique idiopathique révélé par un syndrome hémorragique sévère chez un nourrisson de sept mois. Ann. Fr. Med. Urgence 3, 40–43 (2013). https://doi.org/10.1007/s13341-012-0254-1
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DOI: https://doi.org/10.1007/s13341-012-0254-1