Abstract
A 59-year-old woman presented with sudden-onset eyelid swelling, ptosis, diplopia, mild pulsation, and mild pain of the right periorbital area for 4 days. She had gone to a local hospital and received antihistamine treatment. She was referred to our hospital for further investigation. The patient had no known history of systemic diseases except for hyperlipidemia. She also denied previous trauma and allergies. Her vision was 6/6 in both eyes. Mild lid ptosis was noted in the right side. A Krimsky test revealed a 35-prism diopter of exotropia in the right eye. In addition, extraocular movement showed severe limitations in adduction, supraduction, and infraduction of the right eye (Fig. 27.1). Anterior segments and fundoscopic examination were normal. Pupils were symmetric and reactive to light. An MR imaging study showed an enhancing lesion over the right cavernous sinus (Fig. 27.2) and segmental stenosis of the right internal carotid artery (ICA). The patient was admitted for lumbar puncture which showed an opening and closing pressure of 78/55 mmH2O, respectively. CSF analysis showed no white blood cells and a normal protein level and IgG index (0.64). Pulse therapy with methylprednisolone was given. Her orbital pain was relieved after steroid treatment and eye movement improved gradually. Her eye position returned to orthophoric with a full range of motion observed 1 month later (Fig. 27.3).
Access this chapter
Tax calculation will be finalised at checkout
Purchases are for personal use only
References
İlgen Uslu F, Özkan M. Painful ophthalmoplegia: a case report and literature review. Agri. 2015;27(4):219–23.
Lutt JR, Lim LL, Phal PM, Rosenbaum JT. Orbital inflammatory disease. Semin Arthritis Rheum. 2008;37(4):207–22.
Tolosa E. Periarteritic lesions of the carotid siphon with the clinical features of a carotid infraclinoidal aneurysm. J Neurol Neurosurg Psychiatry. 1954;17(4):300–2.
Hunt WE, Meagher JN, LeFever HE, Zeman W. Painful ophthalmoplegia. Its relation to indolent inflammation of the carvernous sinus. Neurology. 1961;11:56–62.
Kline LB, Hoyt WF. The Tolosa-Hunt syndrome. J Neurol Neurosurg Psychiatry. 2001;71(5):577–82.
Anderson BI. Unusual course of painful ophthalmoplegia. Report of a case. Acta Ophthalmol. 1980;58:841–8.
Kline LB. The Tolosa-Hunt syndrome. Surv Ophthalmol. 1982;27(2):79–95.
Jain R, Sawhney S, Koul RL, Chand P. Tolosa-Hunt syndrome: MRI appearances. J Med Imaging Radiat Oncol. 2008;52(5):447–51.
Author information
Authors and Affiliations
Rights and permissions
Copyright information
© 2018 Springer Nature Singapore Pte Ltd.
About this chapter
Cite this chapter
Wang, AG. (2018). Tolosa-Hunt Syndrome. In: Emergency Neuro-ophthalmology . Springer, Singapore. https://doi.org/10.1007/978-981-10-7668-8_27
Download citation
DOI: https://doi.org/10.1007/978-981-10-7668-8_27
Published:
Publisher Name: Springer, Singapore
Print ISBN: 978-981-10-7667-1
Online ISBN: 978-981-10-7668-8
eBook Packages: MedicineMedicine (R0)